Mitochondrial cytochrome b: evolution and structure of the protein M Degli Esposti, S De Vries, M Crimi, A Ghelli, T Patarnello, A Meyer Biochimica et Biophysica Acta (BBA)-Bioenergetics 1143 (3), 243-271, 1993 | 612 | 1993 |
OPA1 mutations associated with dominant optic atrophy impair oxidative phosphorylation and mitochondrial fusion C Zanna, A Ghelli, AM Porcelli, M Karbowski, RJ Youle, S Schimpf, ... Brain 131 (2), 352-367, 2008 | 416 | 2008 |
pH difference across the outer mitochondrial membrane measured with a green fluorescent protein mutant AM Porcelli, A Ghelli, C Zanna, P Pinton, R Rizzuto, M Rugolo Biochemical and biophysical research communications 326 (4), 799-804, 2005 | 361 | 2005 |
Natural substances (acetogenins) from the family Annonaceae are powerful inhibitors of mitochondrial NADH dehydrogenase (Complex I) M Degli Esposti, A Ghelli, M Ratta, D Cortes, E Estornell Biochemical Journal 301 (1), 161-167, 1994 | 325 | 1994 |
Disruptive mitochondrial DNA mutations in complex I subunits are markers of oncocytic phenotype in thyroid tumors G Gasparre, AM Porcelli, E Bonora, LF Pennisi, M Toller, L Iommarini, ... Proceedings of the National Academy of Sciences 104 (21), 9001-9006, 2007 | 322 | 2007 |
Oestrogens ameliorate mitochondrial dysfunction in Leber’s hereditary optic neuropathy C Giordano, M Montopoli, E Perli, M Orlandi, M Fantin, FN Ross-Cisneros, ... Brain 134 (1), 220-234, 2011 | 276 | 2011 |
Defective oxidative phosphorylation in thyroid oncocytic carcinoma is associated with pathogenic mitochondrial DNA mutations affecting complexes I and III E Bonora, AM Porcelli, G Gasparre, A Biondi, A Ghelli, V Carelli, ... Cancer research 66 (12), 6087-6096, 2006 | 239 | 2006 |
Leber's hereditary optic neuropathy (LHON) pathogenic mutations induce mitochondrial-dependent apoptotic death in transmitochondrial cells incubated with galactose medium A Ghelli, C Zanna, AM Porcelli, AHV Schapira, A Martinuzzi, V Carelli, ... Journal of Biological Chemistry 278 (6), 4145-4150, 2003 | 223 | 2003 |
The effects of idebenone on mitochondrial bioenergetics V Giorgio, V Petronilli, A Ghelli, V Carelli, M Rugolo, G Lenaz, P Bernardi Biochimica et Biophysica Acta (BBA)-Bioenergetics 1817 (2), 363-369, 2012 | 158 | 2012 |
Biochemical features of mtDNA 14484 (ND6/M64V) point mutation associated with Leber's hereditary optic neuropathy V Carelli, A Ghelli, L Bucchi, P Montagna, A De Negri, V Leuzzi, ... Annals of Neurology: Official Journal of the American Neurological …, 1999 | 158 | 1999 |
Leber's hereditary optic neuropathy: biochemical effect of 11778/ND4 and 3460/ND1 mutations and correlation with the mitochondrial genotype V Carelli, A Ghelli, M Ratta, E Bacchilega, S Sangiorgi, R Mancini, ... Neurology 48 (6), 1623-1632, 1997 | 158 | 1997 |
Caspase-independent death of Leber’s hereditary optic neuropathy cybrids is driven by energetic failure and mediated by AIF and Endonuclease G C Zanna, A Ghelli, AM Porcelli, A Martinuzzi, V Carelli, M Rugolo Apoptosis 10, 997-1007, 2005 | 157 | 2005 |
Functional alterations of the mitochondrially encoded ND4 subunit associated with Leber's hereditary optic neuropathy MD Esposti, V Carelli, A Ghelli, M Ratta, M Crimi, S Sangiorgi, ... FEBS letters 352 (3), 375-379, 1994 | 150 | 1994 |
Bioenergetics shapes cellular death pathways in Leber's hereditary optic neuropathy: a model of mitochondrial neurodegeneration V Carelli, M Rugolo, G Sgarbi, A Ghelli, C Zanna, A Baracca, G Lenaz, ... Biochimica et Biophysica Acta (BBA)-Bioenergetics 1658 (1-2), 172-179, 2004 | 147 | 2004 |
Cigarette toxicity triggers Leber’s hereditary optic neuropathy by affecting mtDNA copy number, oxidative phosphorylation and ROS detoxification pathways L Giordano, S Deceglie, P d'Adamo, ML Valentino, C La Morgia, ... Cell death & disease 6 (12), e2021-e2021, 2015 | 140 | 2015 |
The interaction of Q analogs, particularly hydroxydecyl benzoquinone (idebenone), with the respiratory complexes of heart mitochondria M Degli Esposti, A Ngo, A Ghelli, B Benelli, V Carelli, H McLennan, ... Archives of biochemistry and biophysics 330 (2), 395-400, 1996 | 140 | 1996 |
The genetic and metabolic signature of oncocytic transformation implicates HIF1α destabilization AM Porcelli, A Ghelli, C Ceccarelli, M Lang, G Cenacchi, M Capristo, ... Human molecular genetics 19 (6), 1019-1032, 2010 | 139 | 2010 |
The ND1 gene of complex I is a mutational hot spot for Leber's hereditary optic neuropathy ML Valentino, P Barboni, A Ghelli, L Bucchi, C Rengo, A Achilli, A Torroni, ... Annals of Neurology: Official Journal of the American Neurological …, 2004 | 136 | 2004 |
Complex I and complex III of mitochondria have common inhibitors acting as ubiquinone antagonists MD Esposti, A Ghelli, M Crimi, E Estornell, R Fato, G Lenaz Biochemical and biophysical research communications 190 (3), 1090-1096, 1993 | 116 | 1993 |
Respiratory complex I dysfunction due to mitochondrial DNA mutations shifts the voltage threshold for opening of the permeability transition pore toward resting levels AM Porcelli, A Angelin, A Ghelli, E Mariani, A Martinuzzi, V Carelli, ... Biophysical Journal 96 (3), 529a, 2009 | 113 | 2009 |