A new variant of Creutzfeldt-Jakob disease in the UK RG Will, JW Ironside, M Zeidler, K Estibeiro, SN Cousens, PG Smith, ... The Lancet 347 (9006), 921-925, 1996 | 3486 | 1996 |
Updated clinical diagnostic criteria for sporadic Creutzfeldt-Jakob disease I Zerr, K Kallenberg, DM Summers, C Romero, A Taratuto, U Heinemann, ... Brain 132 (10), 2659-2668, 2009 | 971 | 2009 |
Iatrogenic Creutzfeldt–Jakob disease at the millennium P Brown, M Preece, JP Brandel, T Sato, L McShane, I Zerr, A Fletcher, ... Neurology 55 (8), 1075-1081, 2000 | 681 | 2000 |
Analysis of EEG and CSF 14-3-3 proteins as aids to the diagnosis of Creutzfeldt–Jakob disease I Zerr, M Pocchiari, S Collins, JP Brandel, J de Pedro Cuesta, RSG Knight, ... Neurology 55 (6), 811-815, 2000 | 590 | 2000 |
Genetic prion disease: the EUROCJD experience GG Kovács, M Puopolo, A Ladogana, M Pocchiari, H Budka, C van Duijn, ... Human genetics 118, 166-174, 2005 | 469 | 2005 |
Mortality from Creutzfeldt–Jakob disease and related disorders in Europe, Australia, and Canada A Ladogana, M Puopolo, EA Croes, H Budka, C Jarius, S Collins, ... Neurology 64 (9), 1586-1591, 2005 | 440 | 2005 |
Determinants of diagnostic investigation sensitivities across the clinical spectrum of sporadic Creutzfeldt–Jakob disease SJ Collins, P Sanchez-Juan, CL Masters, GM Klug, C van Duijn, ... Brain 129 (9), 2278-2287, 2006 | 361 | 2006 |
Iatrogenic Creutzfeldt-Jakob disease, final assessment P Brown, JP Brandel, T Sato, Y Nakamura, J MacKenzie, RG Will, ... Emerging infectious diseases 18 (6), 901, 2012 | 358 | 2012 |
A test for Creutzfeldt–Jakob disease using nasal brushings CD Orrú, M Bongianni, G Tonoli, S Ferrari, AG Hughson, BR Groveman, ... New England Journal of Medicine 371 (6), 519-529, 2014 | 352 | 2014 |
Predictors of survival in sporadic Creutzfeldt–Jakob disease and other human transmissible spongiform encephalopathies M Pocchiari, M Puopolo, EA Croes, H Budka, E Gelpi, S Collins, V Lewis, ... Brain 127 (10), 2348-2359, 2004 | 303 | 2004 |
Codon 129 prion protein genotype and sporadic Creutzfeldt-Jakob disease. A Alperovitch, I Zerr, M Pocchiari The Lancet 353 (9165), 1673-1674, 1999 | 283 | 1999 |
Incidence and spectrum of sporadic Creutzfeldt–Jakob disease variants with mixed phenotype and co-occurrence of PrPSc types: an updated classification P Parchi, R Strammiello, S Notari, A Giese, JPM Langeveld, A Ladogana, ... Acta neuropathologica 118, 659-671, 2009 | 257 | 2009 |
Efficient transmission and characterization of Creutzfeldt–Jakob disease strains in bank voles R Nonno, MAD Bari, F Cardone, G Vaccari, P Fazzi, G Dell'Omo, ... PLoS pathogens 2 (2), e12, 2006 | 252 | 2006 |
Phenotypic variability of Gerstmann-Sträussler-Scheinker disease is associated with prion protein heterogeneity P Piccardo, SR Dlouhy, PMJ Lievens, K Young, D Phil, TD Bird, D Nochlin, ... Journal of neuropathology and experimental neurology 57 (10), 979-988, 1998 | 241 | 1998 |
Congo red prolongs the incubation period in scrapie-infected hamsters L Ingrosso, A Ladogana, M Pocchiari Journal of virology 69 (1), 506-508, 1995 | 227 | 1995 |
Descriptive epidemiology of Creutzfeldt‐Jakob disease in six european countries, 1993–1995 RG Will, A Alperovitch, S Poser, M Pocchiari, A Hofman, E Mitrova, ... Annals of neurology 43 (6), 763-767, 1998 | 226 | 1998 |
Detection of pathologic prion protein in the olfactory epithelium in sporadic Creutzfeldt–Jakob disease G Zanusso, S Ferrari, F Cardone, P Zampieri, M Gelati, M Fiorini, ... New England Journal of Medicine 348 (8), 711-719, 2003 | 209 | 2003 |
Diagnosis of human prion disease using real-time quaking-induced conversion testing of olfactory mucosa and cerebrospinal fluid samples M Bongianni, C Orrù, BR Groveman, L Sacchetto, M Fiorini, G Tonoli, ... JAMA neurology 74 (2), 155-162, 2017 | 196 | 2017 |
Pre-symptomatic detection of prions by cyclic amplification of protein misfolding C Soto, L Anderes, S Suardi, F Cardone, J Castilla, MJ Frossard, S Peano, ... FEBS letters 579 (3), 638-642, 2005 | 195 | 2005 |
Amphotericin B treatment dissociates in vivo replication of the scrapie agent from PrP accumulation YG Xi, L Ingrosso, A Ladogana, C Masullo, M Pocchiari Nature 356 (6370), 598-601, 1992 | 191 | 1992 |