Neuroprotective effects of iron chelator Desferal on dopaminergic neurons in the substantia nigra of rats with iron-overload H Jiang, Z Luan, J Wang, J Xie Neurochemistry international 49 (6), 605-609, 2006 | 107 | 2006 |
Chaperone Activity of Bicyclic Nojirimycin Analogues for Gaucher Mutations in Comparison with N‐(n‐nonyl)Deoxynojirimycin Z Luan, K Higaki, M Aguilar‐Moncayo, H Ninomiya, K Ohno, ... ChemBioChem 10 (17), 2780-2792, 2009 | 104 | 2009 |
The chaperone activity and toxicity of ambroxol on Gaucher cells and normal mice Z Luan, L Li, K Higaki, E Nanba, Y Suzuki, K Ohno Brain and Development 35 (4), 317-322, 2013 | 100 | 2013 |
A Fluorescent sp2‐Iminosugar With Pharmacological Chaperone Activity for Gaucher Disease: Synthesis and Intracellular Distribution Studies Z Luan, K Higaki, M Aguilar‐Moncayo, L Li, H Ninomiya, E Nanba, ... ChemBioChem 11 (17), 2453-2464, 2010 | 62 | 2010 |
Brainstem neuropathology in a mouse model of Niemann–Pick disease type C Z Luan, Y Saito, H Miyata, E Ohama, H Ninomiya, K Ohno Journal of the neurological sciences 268 (1-2), 108-116, 2008 | 37 | 2008 |
Loss of Na+/K+-ATPase in Drosophila photoreceptors leads to blindness and age-dependent neurodegeneration Z Luan, K Reddig, HS Li Experimental neurology 261, 791-801, 2014 | 35 | 2014 |
Drosophila vision depends on carcinine uptake by an organic cation transporter R Chaturvedi, Z Luan, P Guo, HS Li Cell reports 14 (9), 2076-2083, 2016 | 28 | 2016 |
The putative Na+/Cl−-dependent neurotransmitter/osmolyte transporter inebriated in the Drosophila hindgut is essential for the maintenance of systemic water … Z Luan, C Quigley, HS Li Scientific reports 5 (1), 7993, 2015 | 23 | 2015 |
Inwardly rectifying potassium channels in Drosophila Z Luan, HS Li | 19 | 2012 |
The pharmacological chaperone effect of N-octyl-β-valienamine on human mutant acid β-glucosidases Z Luan, L Li, H Ninomiya, K Ohno, S Ogawa, T Kubo, M Iida, Y Suzuki Blood Cells, Molecules, and Diseases 44 (1), 48-54, 2010 | 17 | 2010 |
The effect of N-octyl-β-valienamine on β-glucosidase activity in tissues of normal mice Z Luan, H Ninomiya, K Ohno, S Ogawa, T Kubo, M Iida, Y Suzuki Brain and Development 32 (10), 805-809, 2010 | 11 | 2010 |
Chemical chaperone therapy: Luciferase assay for screening of β-galactosidase mutations L Li, K Higaki, H Ninomiya, Z Luan, M Iida, S Ogawa, Y Suzuki, K Ohno, ... Molecular genetics and metabolism 101 (4), 364-369, 2010 | 8 | 2010 |
Mental retardation, spasticity, basal ganglia calcification, cerebral white matter lesions, multiple endocrine defects, telangiectasia and atrophic skin: A new syndrome? Y Saito, M Toyoshima, A Oka, L Zhuo, S Moriwaki, O Yamamoto, ... Brain and Development 30 (3), 221-225, 2008 | 1 | 2008 |
CHEMICAL CHAPERONE THERAPY FOR GAUCHER DISEASE: N-OCTYL-BETA-VALIENAMINE INCREASES THE CELLULAR ACTIVITY OF NOT ONLY F213I BUT ALSO N188S BETAGLUCOCEREBROSIDASES K Ohno, K Lei, Z Luan, T Inoue, H Ninomiya, E Nanba, Y Suzuki Neuropediatrics 37 (S 1), PS1_3_6, 2006 | | 2006 |
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